Ovotesticular Differences of Sex Development

**Semantic type:** Congenital Abnormality|Disease or Syndrome

**Definition:** Difference of sex development characterized by the presence of ovarian and testicular tissue in the same individual. The clinical manifestations of the condition, which can be associated with 46,XX, 46,XY or 46,XX/46,XY mosaic karyotype, are variable.

**Synonyms:** - Ovotesticular DSD - Ovotesticular Disorders of Sex Development - True Hermaphroditism