Central Nervous System Embryonal Tumor with Rhabdoid Features

**Semantic type:** Neoplastic Process

**Definition:** A central nervous system embryonal neoplasm characterized by the presence of histological features consistent with atypical teratoid/rhabdoid tumor and absence of mutations of the INI1 gene or SMARCA4 (BRG1) gene.

**Synonyms:** - CNS Embryonal Tumor with Rhabdoid Features - CNS Embryonal tumor with rhabdoid features