World Of Taxonomy
C131425Level 8

Congenital Hyperinsulinism

**Semantic type:** Disease or Syndrome

**Definition:** An etiologically heterogenous condition resulting in dysregulated insulin secretion whose cause is present from birth. It is the most common cause of persistent hypoglycemia in neonates, infants and children.

**Synonyms:** - HHI - Hyperinsulinemia of Infancy - Hyperinsulinemic Hypoglycemia - Neonatal Hyperinsulinism - Nesidioblastosis

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