Congenital Peribronchial Myofibroblastic Tumor

**Semantic type:** Neoplastic Process

**Definition:** A rare lung neoplasm that occurs in the intrauterine and perinatal period. It is characterized by the proliferation of spindle cells in an interstitial, peribronchial pattern. Surgical resection of the involved lung parenchyma is the treatment of choice.

**Synonyms:** - Congenital Bronchopulmonary Leiomyosarcoma - Congenital Fibrosarcoma - Congenital Mesenchymal Malformation of Lung - Congenital Pulmonary Myofibroblastic Tumor - Congenital peribronchial myofibroblastic tumor - Neonatal Pulmonary Hamartoma