Primary Pulmonary Myxoid Sarcoma with EWSR1-CREB1 Fusion

**Semantic type:** Neoplastic Process

**Definition:** A sarcoma that arises from the lung. It is related to a bronchus and is often predominantly endobronchial. It is characterized by the proliferation of round and spindle cells within a myxoid stroma. It is associated with the presence of an EWSR1::CREB1 fusion gene.

**Synonyms:** - Low-Grade Malignant Myxoid Endobronchial Tumor - PPMS - Primary Pulmonary Myxoid Sarcoma - Primary Pulmonary Myxoid Sarcoma with EWSR1::CREB1 Fusion - Pulmonary Myxoid Sarcoma with EWSR1-CREB1 Translocation - Pulmonary myxoid sarcoma with EWSR1-CREB1 translocation