Fibrocystin

**Semantic type:** Amino Acid, Peptide, or Protein

**Definition:** Fibrocystin (4074 aa, ~447 kDa) is encoded by the human PKHD1 gene. This protein may be involved in receptor signaling that promotes differentiation of the kidney and biliary system.

**Synonyms:** - PKHD1 - Polycystic Kidney and Hepatic Disease 1 Protein - Polyductin - Tigmin