World Of Taxonomy
C152045Level 6

Delta-1-Pyrroline-5-Carboxylate Dehydrogenase, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (563 aa, ~62 kDa) is encoded by the human ALDH4A1 gene. This protein is involved in the conversion of proline pyrroline-5-carboxylate to glutamate.

**Synonyms:** - ALDH4A1 - Aldehyde Dehydrogenase 4 - Aldehyde Dehydrogenase 4 Family Member A1 - Aldehyde Dehydrogenase Family 4 Member A1 - EC 1.2.1.88 - L-Glutamate Gamma-Semialdehyde Dehydrogenase - Mitochondrial Delta-1-Pyrroline 5-Carboxylate Dehydrogenase - P5C Dehydrogenase - Pyrroline-5-Carboxylate Dehydrogenase

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