C155319Level 5
Pyruvate Dehydrogenase Protein X Component, Mitochondrial
**Semantic type:** Amino Acid, Peptide, or Protein
**Definition:** Pyruvate dehydrogenase protein X component, mitochondrial (501 aa, ~54 kDa) is encoded by the human PDHX gene. This protein plays a role in anchoring dihydrolipoamide dehydrogenase (E3) to the dihydrolipoamide transacetylase (E2) core of the pyruvate dehydrogenase complex.
**Synonyms:** - Dihydrolipoamide Dehydrogenase-Binding Protein of Pyruvate Dehydrogenase Complex - E3-Binding Protein - E3BP - Lipoyl-Containing Pyruvate Dehydrogenase Complex Component X - PDHX - Pyruvate Dehydrogenase Complex, E3-Binding Protein Subunit - Pyruvate Dehydrogenase Complex, Lipoyl-Containing Component X - proX
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