EBV-Related Lymphoproliferative Disease with Primary Immunodeficiency

**Semantic type:** Disease or Syndrome

**Definition:** An EBV-related lymphoid proliferation that arises in the setting of immune deficiency due to a primary immunodeficiency or immunoregulatory disorder.

**Synonyms:** - EBV- Associated Lymphoproliferative Disease with Primary Immunodeficiency - Epstein-Barr Virus-Related Lymphoproliferative Disease with Primary Immunodeficiency