Primary Uveal Non-Hodgkin Lymphoma

**Semantic type:** Neoplastic Process

**Definition:** An indolent, low-grade B-cell non-Hodgkin lymphoma that arises from the choroid, iris, or ciliary body. It is characterized by the presence of a diffuse infiltrate of small, round lymphocytes. Lymphoid follicles with germinal centers may be present. In the past these tumors were termed 'reactive lymphoid hyperplasia'. Now they are considered low-grade B-cell lymphomas, most commonly extranodal marginal zone lymphomas of mucosa-associated lymphoid tissue.

**Synonyms:** - Primary Uveal Lymphoma - Uveal Reactive Lymphoid Hyperplasia