Desmoplastic Myxoid Tumor of the Pineal Region, SMARCB1-Mutant

**Semantic type:** Neoplastic Process

**Definition:** A SMARCB1-deficient tumor of the brain arising in the pineal region. It is characterized by the presence of spindled and epithelioid cells with low-grade morphology that are embedded in a desmoplastic stroma alternating with various extents of loose myxoid matrix.

**Synonyms:** - Desmoplastic Myxoid Tumor, SMARCB1-Mutant