Otosclerosis

**Semantic type:** Disease or Syndrome

**Definition:** A usually autosomal dominant inherited metabolic disorder affecting the bony labyrinth of the inner ear. Morphologically, it is characterized by the presence of sharply demarcated active (otospongiotic) and inactive (sclerotic) bony areas. It is one of the most common causes of conductive hearing loss.

**Synonyms:** - Localized Bone Dysplasia