C186489Level 7
Carnitine O-Palmitoyltransferase 1, Liver Isoform
**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme
**Definition:** Carnitine O-palmitoyltransferase 1, liver isoform (773 aa, ~88 kDa) is encoded by the human CPT1A gene. This protein is involved in both hepatic triglyceride metabolism and the transfer of the acyl group of long-chain fatty acid-CoA conjugates onto carnitine, which facilitates mitochondrial uptake.
**Synonyms:** - CPT I - CPT IA - CPT1-Alpha - CPT1-L - CPT1A - CPTI-L - Carnitine O-Palmitoyltransferase I, Liver Isoform - Carnitine Palmitoyltransferase 1A - Carnitine Palmitoyltransferase IA - EC 2.3.1.21
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Cross-system equivalences0
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