Embryonal Tumor with Multilayered Rosettes

**Semantic type:** Neoplastic Process

**Definition:** A central nervous system embryonal tumor characterized by the presence of multilayered rosette formation and typically the presence of amplification of the C19MC region on chromosome 19 (19q13.42) or rarely a DICER1 mutation.

**Synonyms:** - ETMR - Embryonal Tumor with Multilayered Rosettes, NOS