Central Nervous System Neuroblastoma, FOXR2-Activated

**Semantic type:** Neoplastic Process

**Definition:** A rare central nervous system neoplasm with neuroblastic and/or neuronal differentiation that arises from the supratentorial brain. It is characterized by the presence of structural rearrangements of FOXR2 gene that result in the activation of the transcription factor FOXR2.

**Synonyms:** - CNS Neuroblastoma, FOXR2-Activated - Central Nervous System Neuroblastoma - Central Nervous System Neuroblastoma - Central Neuroblastoma - Cerebral Neuroblastoma