Pyruvate Carboxylase, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Pyruvate carboxylase, mitochondrial (1178 aa, ~130 kDa) is encoded by the human PC gene. This protein is involved in catalyzing the carboxylation of pyruvate to oxaloacetate.

**Synonyms:** - EC 6.4.1.1 - PC - PCB - Pyruvate Carboxylase - Pyruvic Carboxylase