Methylcrotonoyl-CoA Carboxylase Beta Chain, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial (563 aa, ~61 kDa) is encoded by the human MCCC2 gene. This protein is involved in catalyzing the carboxylation of 3-methylcrotonyl-CoA to yield 3-methylglutaconyl-CoA.

**Synonyms:** - 3-Methylcrotonyl-CoA Carboxylase 2 - 3-Methylcrotonyl-CoA Carboxylase Non-Biotin Containing Subunit - 3-Methylcrotonyl-CoA Carboxylase Non-Biotin-Containing Subunit - 3-Methylcrotonyl-CoA:Carbon Dioxide Ligase Subunit Beta - EC 6.4.1.4 - MCCC2 - MCCase Subunit Beta - Methylcrotonoyl-CoA Carboxylase 2 - Methylcrotonoyl-CoA Carboxylase Beta - Testicular Secretory Protein Li 29