Isovaleryl-CoA Dehydrogenase, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Isovaleryl-CoA dehydrogenase, mitochondrial (426 aa, ~47 kDa) is encoded by the human IVD gene. This protein is involved in the conversion of isovaleryl-CoA/3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA.

**Synonyms:** - Butyryl-CoA Dehydrogenase - EC 1.3.8.1 - EC 1.3.8.4 - IVD - Isovaleryl-CoA Dehydrogenase - Isovaleryl-Coenzyme A Dehydrogenase