Alpha-Aminoadipic Semialdehyde Synthase, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Alpha-aminoadipic semialdehyde synthase, mitochondrial (926 aa, ~102 kDa) is encoded by the human AASS gene. This protein plays a role in the two step conversion of lysine to alpha-aminoadipic semialdehyde.

**Synonyms:** - AASS - Alpha-Aminoadipate Semialdehyde Synthase - Alpha-Aminoadipic Semialdehyde Synthase - Aminoadipate-Semialdehyde Synthase - LKR/SDH - Lysine Ketoglutarate Reductase/Saccharopine Dehydrogenase - Lysine-Ketoglutarate Reductase/Saccharopine Dehydrogenase