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C199258Level 10

B Acute Lymphoblastic Leukemia with UBTF-ATXN7L3/PAN3, CDX2 ("CDX2/UBTF")

**Semantic type:** Neoplastic Process

**Definition:** B acute lymphoblastic leukemia associated with concomitant CDX2 deregulation and expression of the chimeric UBTF-ATXN7L3 fusion oncoprotein. It usually affects female adolescents and young adults. The prognosis is poor following treatment with conventional chemotherapy.

**Synonyms:** - B Acute Lymphoblastic Leukemia, CDX2-Deregulated, UBTF-ATXN7L3 Rearranged - B Acute Lymphoblastic Leukemia, CDX2-Deregulated, UBTF::ATXN7L3 Rearranged - B Acute Lymphoblastic Leukemia, CDX2/UBTF-Deregulated - B-ALL with UBTF-ATXN7L3/PAN3, CDX2 ("CDX2/UBTF") - B-ALL with UBTF::ATXN7L3/PAN3, CDX2 ("CDX2/UBTF") - B-ALL, CDX2-Deregulated, UBTF-ATXN7L3 Rearranged - B-ALL, CDX2-Deregulated, UBTF::ATXN7L3 Rearranged - B-ALL, CDX2/UBTF-Deregulated - B-Acute Lymphoblastic Leukemia with UBTF-ATXN7L3/PAN3, CDX2 ("CDX2/UBTF") - B-Acute Lymphoblastic Leukemia, CDX2-Deregulated, UBTF-ATXN7L3 Rearranged - B-Acute Lymphoblastic Leukemia, CDX2-Deregulated, UBTF::ATXN7L3 Rearranged - B-Acute Lymphoblastic Leukemia, CDX2/UBTF-Deregulated

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