Indolent NK-Cell Lymphoproliferative Disorder of the Gastrointestinal Tract

**Semantic type:** Disease or Syndrome

**Definition:** An indolent lymphoproliferative disorder that affects the gastrointestinal tract. The neoplastic lymphocytes have the typical phenotype of NK-cells, are of medium to large size, show mild pleomorphism, and are EBV infection negative. Features that characterize extranodal NK/T-cell lymphomas (e.g., angioinvasion and angiodestruction) are not present.

**Synonyms:** - Lymphomatoid Gastropathy - NK-Cell Enteropathy - NKCE