Ubiquinone Biosynthesis Monooxygenase COQ6, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Ubiquinone biosynthesis monooxygenase COQ6, mitochondrial (468 aa, ~51 kDa) is encoded by the human COQ6 gene. This protein plays a role in the hydroxylation of 3-hexaprenyl-4-hydroxybenzoic acid (HHB) to 3-hexaprenyl-4,5-dihydroxybenzoic acid (DHHB).

**Synonyms:** - COQ6 - Coenzyme Q10 Monooxygenase 6 - EC 1.14.13.-