Enoyl-CoA Hydratase, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Enoyl-CoA hydratase, mitochondrial (290 aa, ~31 kDa) is encoded by the human ECHS1 gene. This protein plays a role in valine metabolism and the hydration of 2-trans-enoyl-coenzyme A (CoA) intermediates to L-3-hydroxyacylated forms of coenzyme A.

**Synonyms:** - EC 4.2.1.17 - EC 5.3.3.8 - ECHS1 - Enoyl-CoA Hydratase 1 - SCEH - Short-Chain Enoyl-CoA Hydratase - mECH - mECH1