Frataxin, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Frataxin, mitochondrial (210 aa, ~23 kDa) is encoded by the human FXN gene. This protein is involved in [2Fe-2S] cluster biogenesis and heme biosynthesis.

**Synonyms:** - EC 1.16.3.1 - FXN - Frataxin - Friedreich Ataxia Protein - Fxn