Hydroxyacyl-Coenzyme A Dehydrogenase, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial (314 aa, ~34 kDa) is encoded by the human HADH gene. This protein plays a role in beta-oxidation of fatty acids and the modulation of insulin secretion through the regulation of glutamate dehydrogenase 1 activity.

**Synonyms:** - EC 1.1.1.35 - HADH - HCDH - Hydroxyacyl-CoA Dehydrogenase - Hydroxyacyl-Coenzyme A Dehydrogenase - Medium and Short-Chain L-3-Hydroxyacyl-Coenzyme A Dehydrogenase - Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase - Testis Secretory Sperm-Binding Protein Li 203a