C201712Level 6
Trifunctional Enzyme Subunit Alpha, Mitochondrial
**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme
**Definition:** Trifunctional enzyme subunit alpha, mitochondrial (763 aa, ~83 kDa) is encoded by the human HADHA gene. This protein is involved in the metabolism of long-chain fatty acids.
**Synonyms:** - 78 kDa Gastrin-Binding Protein - EC 4.2.1.17/EC 1.1.1.211 - HADHA - Hydroxyacyl-CoA Dehydrogenase Trifunctional Multienzyme Complex Subunit Alpha - Long-Chain Enoyl-CoA Hydratase/Long Chain 3-Hydroxyacyl-CoA Dehydrogenase - Monolysocardiolipin Acyltransferase - TP-Alpha
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