Pineoblastoma miRNA Processing Altered 1

**Semantic type:** Neoplastic Process

**Definition:** Pineoblastoma characterized by alterations in genes involved in miRNA biogenesis (DICER1, DROSHA, and DGCR8). It may manifest as a sporadic tumor or part of DICER1 syndrome. It affects children.

**Synonyms:** - PB-miRNA1 - Pineoblastioma-miRNA1 - Pineoblastoma miRNA Processing Altered Group 1