Pineoblastoma miRNA Processing Altered 2

**Semantic type:** Neoplastic Process

**Definition:** Pineoblastoma characterized by alterations in genes involved in miRNA biogenesis (DICER1, DROSHA, and DGCR8). It may manifest as a sporadic tumor or part of DICER1 syndrome. It affects older children and follows a more favorable course.

**Synonyms:** - PB-miRNA2 - Pineoblastioma-miRNA2 - Pineoblastoma miRNA Processing Altered Group 2