World Of Taxonomy
C201973Level 11

Pineoblastoma, MYC/FOXR2-Activated

**Semantic type:** Neoplastic Process

**Definition:** Pineoblastoma characterized by MYC activation, chromosome 16 losses, and overexpression of FOXR2. It affects young children and is associated with a dismal prognosis.

**Synonyms:** - PB, MYC-Altered - PB, MYC/FOXR2-Activated - PB, MYC/FOXR2-Altered - PB-MYC - PB-MYC/FOXR2 - Pineoblastoma, MYC-Altered - Pineoblastoma, MYC/FOXR2-Altered - Pineoblastoma-MYC - Pineoblastoma-MYC/FOXR2

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