Gigantiform Cementoma

**Semantic type:** Disease or Syndrome

**Definition:** An extremely rare, benign, rapidly progressing fibro-osseous lesion that arises from the jaws as a multifocal expansile growth in children or adolescents. It results in significant deformity, orbital distortion, and possible airway involvement. An autosomal dominant inheritance has been proposed. Histologically, it is characterized by the presence of immature bony trabeculae and cementum-like calcifications within a hypercellular fibroblastic stroma. It shares morphological features with florid cemento-osseous dysplasia, but in florid cemento-osseous dysplasia the degree of expansion is less prominent and patients are usually older.

**Synonyms:** - Expansive Osseous Dysplasia - FGC - Familial Gigantiform Cementoma - Florid Osseous Dysplasia - Florid osseous dysplasia - Gigantiform cementoma