N-Acetylglutamate Synthase, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** N-acetylglutamate synthase, mitochondrial (534 aa, ~58 kDa) is encoded by the human NAGS gene. This protein is involved in the formation of N-acetylglutamate (NAG) from glutamate and acetyl coenzyme-A (CoA).

**Synonyms:** - Amino-Acid Acetyltransferase - EC 2.3.1.1 - N-Acetylglutamate Synthase - NAGS