Phytanoyl-CoA Dioxygenase, Peroxisomal

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Phytanoyl-CoA dioxygenase, peroxisomal (338 aa, ~39 kDa) is encoded by the human PHYH gene. This protein is involved in the 2-hydroxylation of racemic phytanoyl-CoA, isomers of 3-methylhexadecanoyl-CoA and a variety of other mono-branched 3-methylacyl-CoA esters and straight-chain acyl-CoA esters.

**Synonyms:** - EC 1.14.11.18 - PHYH - PhyH - Phytanic Acid Oxidase - Phytanoyl-CoA 2-Hydroxylase - Phytanoyl-CoA Alpha-Hydroxylase - Phytanoyl-CoA Dioxygenase