World Of Taxonomy
C213036Level 13

Von Hippel Lindau Syndrome-Associated Clear Cell Renal Cell Carcinoma

**Semantic type:** Neoplastic Process

**Definition:** A clear cell renal cell carcinoma that develops in a patient with Von Hippel Lindau syndrome. Renal involvement in Von Hippel Lindau syndrome is characterized by multiple, bilateral, and recurring tumors.

**Synonyms:** - Von Hippel Lindau Syndrome-Associated Clear Cell RCC - Von Hippel-Lindau Syndrome-Associated Clear Cell RCC - Von Hippel-Lindau Syndrome-Associated Clear Cell Renal Cell Carcinoma

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