Oxygen-Dependent Coproporphyrinogen-III Oxidase, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Oxygen-dependent coproporphyrinogen-III oxidase, mitochondrial (454 aa, ~50 kDa) is encoded by the human CPOX gene. This protein is involved in the oxidative decarboxylation of coproporphyrinogen III to yield protoporphyrinogen IX.

**Synonyms:** - COX - CPOX - Coprogen Oxidase - Coproporphyrinogen Oxidase - Coproporphyrinogenase - EC 1.3.3.3