D-2-Hydroxyglutarate Dehydrogenase, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** D-2-hydroxyglutarate dehydrogenase, mitochondrial (521 aa, ~56 kDa) is encoded by the human D2HGDH gene. This protein plays a role in the interconversion of D-2-hydroxyglutarate (D-2-HG) to alpha-ketoglutarate.

**Synonyms:** - D-2-Hydroxyglutarate Dehydrogenase - D2HGDH - EC 1.1.99.39