Lipoamide Acyltransferase Component of Branched-Chain Alpha-Keto Acid Dehydrogenase Complex, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial (482 aa, ~54 kDa) is encoded by the human DBT gene. This protein is involved in catalyzing coenzyme A transfer during branched-chain alpha-keto acid metabolism.

**Synonyms:** - 52 kDa Mitochondrial Autoantigen of Primary Biliary Cirrhosis - BCKAD-E2 - BCKADE2 - BCKDH-E2 - BCOADC-E2 - Branched Chain 2-Oxo-Acid Dehydrogenase Complex Component E2 - Branched-Chain Alpha-Keto Acid Dehydrogenase Complex Component E2 - DBT - Dihydrolipoamide Acetyltransferase Component of Branched-Chain Alpha-Keto Acid Dehydrogenase Complex - Dihydrolipoamide Branched Chain Transacylase - Dihydrolipoamide Branched Chain Transacylase E2 - Dihydrolipoamide Branched-Chain Transacylase - Dihydrolipoyl Transacylase - Dihydrolipoyllysine-Residue (2-Methylpropanoyl)Transferase - EC 2.3.1.168