Glutaryl-CoA Dehydrogenase, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Glutaryl-CoA dehydrogenase, mitochondrial (438 aa, ~48 kDa) is encoded by the human GCDH gene. This protein plays a role in oxidative decarboxylation of glutaryl-CoA to crotonyl-CoA during the degradation of certain amino acids.

**Synonyms:** - EC 1.3.8.6 - GCD - GCDH - Glutaryl-CoA Dehydrogenase - Glutaryl-Coenzyme A Dehydrogenase - Glutaryl-Coenzyme A Dehydrogenase, Mitochondrial