Necrobiotic Xanthogranuloma

**Semantic type:** Disease or Syndrome

**Definition:** A rare, chronic, progressive non-Langerhans cell histiocytosis of the skin characterized by the presence of yellow-to-orange papules, nodules, or plaques on the skin, usually in the periorbital area. It is frequently associated with monoclonal gammopathy.

**Synonyms:** - NXG