C219945Level 9
Fibrocalculous Pancreatic Diabetes
**Semantic type:** Disease or Syndrome
**Definition:** An uncommon form of diabetes mellitus that is ketosis-resistant and associated with pancreatic abnormalities that include large intraductal calculi and fibrosis progressing to exocrine and endocrine pancreatic failure. Patients are commonly young, normal weight, and originate from tropical countries.
**Synonyms:** - Fibrocalculous pancreatic diabetes
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