Propionyl-CoA Carboxylase Beta Chain, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Propionyl-CoA carboxylase beta chain, mitochondrial (539 aa, ~58 kDa) is encoded by the human PCCB gene. This protein plays a role in the transfer of a carboxyl group from a biotin carrier to either butynyl- or propionyl-CoA to form ethylmalonyl- or methylmalonyl-CoA.

**Synonyms:** - EC 6.4.1.3 - PCCB - PCCase Beta Subunit - PCCase Subunit Beta - Propanoyl-CoA:Carbon Dioxide Ligase Beta Subunit - Propanoyl-CoA:Carbon Dioxide Ligase Subunit Beta - Propionyl-CoA Carboxylase Beta Chain