Proximal-Type Epithelioid Sarcoma

**Semantic type:** Neoplastic Process

**Definition:** An epithelioid sarcoma predominantly involving the pelvis, perineum, and genital organs. It tends to have a more aggressive clinical course as compared to the more frequently seen distal-type epithelioid sarcoma.

**Synonyms:** - Central Epithelioid Sarcoma - Large Cell Epithelioid Sarcoma - Proximal Epithelioid Sarcoma