C3444Level 6
Granulomatosis with Polyangiitis
**Semantic type:** Disease or Syndrome
**Definition:** A rare, autoimmune, systemic medium and small size vasculitis. It is characterized by the formation of necrotizing granulomas in the respiratory tract, necrotizing angiitis, and glomerulonephritis.
**Synonyms:** - GPA - GPA - Wegener Granulomatosis - Wegener Granulomatosis - Wegener's Granulomatosis - Wegener's Granulomatosis
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