C35288Level 10
Desquamative Interstitial Pneumonia
**Semantic type:** Disease or Syndrome
**Definition:** A rare idiopathic interstitial pneumonia characterized by accumulation of macrophages in alveolar spaces and interstitial inflammation. It usually occurs in smokers. Some patients develop progressive interstitial lung fibrosis.
**Synonyms:** - DIP - RBILD - Respiratory Bronchiolitis Interstitial Lung Disease
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