World Of Taxonomy
C35288Level 10

Desquamative Interstitial Pneumonia

**Semantic type:** Disease or Syndrome

**Definition:** A rare idiopathic interstitial pneumonia characterized by accumulation of macrophages in alveolar spaces and interstitial inflammation. It usually occurs in smokers. Some patients develop progressive interstitial lung fibrosis.

**Synonyms:** - DIP - RBILD - Respiratory Bronchiolitis Interstitial Lung Disease

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