Malignant Peripheral Nerve Sheath Tumor

**Semantic type:** Neoplastic Process

**Definition:** An uncommon, highly aggressive malignant tumor, arising from the peripheral nerves and affecting mostly adults in their third to sixth decades of life. It usually occurs in medium-sized and large nerves of the buttock, thigh, upper arm, or the paraspinal region. It may be associated with neurofibromatosis 1 (NF1).

**Synonyms:** - MPNST - MPNST - MPNST, NOS - Malig. periph. nerve sheath tum. - Malignant Neurilemmoma - Malignant Neurilemmoma - Malignant Peripheral Nerve Sheath Neoplasm - Malignant Peripheral Nerve Sheath Tumour - Malignant Schwannoma - Malignant peripheral nerve sheath tumor - Malignant peripheral nerve sheath tumor - Neurilemoma, malignant - Neurofibrosarcoma - Neurofibrosarcoma - Neurofibrosarcoma, Malignant - Neurogenic sarcoma - SCHWANNOMA, MALIGNANT - malignant peripheral nerve sheath tumor