Rhabdoid Tumor

**Semantic type:** Neoplastic Process

**Definition:** An aggressive malignant embryonal neoplasm usually occurring during childhood. It is characterized by the presence of large cells with abundant cytoplasm, large eccentric nucleus, and a prominent nucleolus and it is associated with abnormalities of chromosome 22. It can arise from the central nervous system, kidney, and the soft tissues. The prognosis is poor.

**Synonyms:** - Rhabdoid Sarcoma - Rhabdoid sarcoma - Rhabdoid tumor, NOS - rhabdoid tumor