Lung Lymphangioleiomyomatosis

**Semantic type:** Neoplastic Process

**Definition:** Lymphangiomyomatosis involving the lungs and local lymph nodes. Patients usually present with chylous pleural effusion. The clinical course is variable. Patients with resectable lesions usually have a favorable clinical outcome. Patients with diffuse lesions usually have a progressive clinical course.

**Synonyms:** - Lung Lymphangiomyomatosis