Melanoma Arising in Giant Congenital Nevus

**Semantic type:** Neoplastic Process

**Definition:** A melanoma arising in a giant congenital melanocytic nevus. The risk of developing a melanoma in a giant congenital melanocytic nevus has been reported to be between 5% and 50%. The incidence of developing melanoma is higher before the age of 10 and in adult life.

**Synonyms:** - Malignant melanoma in congenital melanocytic nevus - Malignant melanoma in giant pigmented nevus