Clear Cell Sarcoma of the Kidney

**Semantic type:** Neoplastic Process

**Definition:** A rare pediatric sarcoma affecting the kidney. It is characterized by the presence of epithelioid or spindle cells forming cords or nests, separated by fibrovascular septa. It metastasizes to lung, bone, brain and soft tissue.

**Synonyms:** - CCSK - Childhood Clear Cell Sarcoma of the Kidney - Childhood Kidney Clear Cell Sarcoma - Childhood Renal Clear Cell Sarcoma - Clear Cell Sarcoma of Kidney - Clear cell sarcoma - kidney - Clear cell sarcoma of kidney - Clear cell sarcoma of the kidney - Clear cell sarcoma of the kidney (CCSK) - Kidney Clear Cell Sarcoma - Pediatric Kidney Clear Cell Sarcoma - Pediatric Renal Clear Cell Sarcoma - Renal Clear Cell Sarcoma - clear cell sarcoma of the kidney