Desmoplastic Infantile Ganglioglioma

**Semantic type:** Neoplastic Process

**Definition:** A WHO grade I large cystic tumor that occurs almost exclusively in infants, with a prominent desmoplastic stroma having a neuroepithelial population of neoplastic astrocytes together with a variable neuronal component. It involves the superficial cerebral cortex and leptomeninges, and often attaches to the dura. Although clinically it presents as a large tumor, it generally has a good prognosis following surgical resection. (Adapted from WHO)

**Synonyms:** - DIG - Desmoplastic infantile ganglioglioma