Porokeratotic Eccrine Ostial and Dermal Duct Nevus

**Semantic type:** Disease or Syndrome

**Definition:** A rare, congenital disorder of the eccrine sweat ducts that presents as grouped keratotic papules and plaques with a linear distribution and/or multiple punctate pits filled with tiny keratotic plugs resembling comedones. The lesion are usually located on the acral portion of a limb.

**Synonyms:** - Linear Eccrine Nevus with Comedones - Porokeratotic Eccrine Duct and Hair Follicle Nevus